Hamartoma of the mitral valve with blood cysts: a rare tumor detected by echoca...

• Author(s): Abreu, A ; Galrinho, A ; Sá, E ; Ramos, S ; Martins, A ; Fragata, J ; Ferreira, R
• Date: 1998
• Persistent ID: http://hdl.handle.net/10400.10/748
• Origin: Repositório do Hospital Prof. Doutor Fernando Fonseca
• Subject(s): Neoplasias do coração; Hamartoma; Válvula mitral; Ecocardiografia; Heart Neoplasms; Mitral Valve; Echocardiography
• Document Type: Article
• Language: English

Description

A 16-year-old boy was submitted to a cardiac examination after an episode of faintness. A transthoracic echocardiogram was performed, which revealed a very mobile multicystic tumor attached to the mitral valve. A small solid mass adherent to the cysts was better defined by transesophageal echocardiography. The patient was submitted to cardiac surgery consisting of tumor resection and a mitral prosthesis implant. The surgery was successful. The tumor consisted of three bright red tense cysts with hematic content, each 1 to 2 cm in diameter. The cysts were coalescent and adherent to a solid mass attached to the posterior papillary muscle head. Histopathologic examination revealed a hamartoma with a cystic part composed of the proliferation of myofibroblast cells in a stroma with vessels, collagen, and elastin fibers. Valvular hamartoma with blood cysts is a very rare cardiac tumor both for its histopathology and its localization.