Document details

Case for diagnosis

Author(s): Fernandes, I. cv logo 1 ; Sanches, M. cv logo 2 ; Alves, R. cv logo 3 ; Selores, M. cv logo 4

Date: 2012

Persistent ID: http://hdl.handle.net/10400.16/1351

Origin: Repositório Científico do Centro Hospitalar do Porto


Description
Abstract We report a clinical case of a rare variant of pemphigus - pemphigus herpetiformis - which combines the clinical features of dermatitis herpetiformis with the immunological findings of pemphigus. Due to its atypical presentation, it is frequently misdiagnosed as dermatitis herpetiformis. It is basically characterized by the herpetiform pattern of skin lesions, severe pruritus and by the presence of eosinophilic spongiosis confirmed on histopathology. We call attention to the excellent response to dapsone.
Document Type Article
Language English
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Fundação para a Ciência e a Tecnologia Universidade do Minho   Governo Português Ministério da Educação e Ciência Programa Operacional da Sociedade do Conhecimento EU