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Neuropathy in Waldenstrom's macroglobulinemia.

Coimbra, J; Serviço de Neurologia, Hospital Garcia de Orta, Almada.; Costa, A P; Pita, F; Rosado, P; de Almeida, L B

The association of a neuropathy and a paraproteinaemia such as Waldenström's macroglobulinaemia is frequent and not fortuitous. This paper reports a slowly progressive, predominantly sensory neuropathy, occurring in a 69-year-old man, as the first sign of a Waldenström's macroglobulinaemia. A saphenous [correction of sural] nerve biopsy revealed a mixed process of primary demyelination and axonal degeneration. ...

Data: 1970   |   Origem: Acta Médica Portuguesa

Familial peripheral neuropathy caused by susceptibility to entrapment (tomaculo...

Viana, J P; Serviço de Neurologia, Hospital de Santo António dos Capuchos, Lisboa.; Coimbra, J; Goulart, Z; de Almeida, L B; Beirão, J C

The authors describe a case of hereditary neuropathy with liability to pressure palsies (entrapment), and compare it to reports from literature. The main characteristics are: autosomal dominant inheritance, recurrent mononeuropathies (ulnar, median, peroneal, brachial plexus), and specific features at nerve biopsy. The sensory nerve reveals predominantly demyelinating alterations, having the remaining myelin fi...

Data: 1970   |   Origem: Acta Médica Portuguesa

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Fundação para a Ciência e a Tecnologia Universidade do Minho   Governo Português Ministério da Educação e Ciência Programa Operacional da Sociedade do Conhecimento União Europeia