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Measurements of CFTR-Mediated Cl- Secretion in Human Rectal Biopsies Constitute...

Sousa, Marisa; Servidoni, Maria F.; Vinagre, Adriana M.; Ramalho, Anabela S.; Bonadia, Luciana C.; Felício, Verónica; Ribeiro, Maria A..

BACKGROUND: Cystic Fibrosis (CF) is caused by ∼1,900 mutations in the CF transmembrane conductance regulator (CFTR) gene encoding for a cAMP-regulated chloride (Cl(-)) channel expressed in several epithelia. Clinical features are dominated by respiratory symptoms, but there is variable organ involvement thus causing diagnostic dilemmas, especially for non-classic cases. METHODOLOGY/PRINCIPAL FINDINGS: To furth...


Mean distance of closest approach of ions: Sodium salts in aqueous solutions

Ribeiro, Ana C. F.; Esteso, Miguel A.; Lobo, Victor M. M.; Burrows, Hugh D.; Amado, Ana M.; Costa, António M. Amorim da; Sobral, Abílio J. F. N.

The estimation of numerical values for the mean distance of closest approach of ions, a, of sodium salts in aqueous solutions, determined from activity and diffusion coefficients, and also from different theoretical approaches, is presented and discussed. ; http://www.sciencedirect.com/science/article/B6TGR-4JCCFW7-1/1/45bf32523013b068b5040514add5505a


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