Encontrados 131 documentos, a visualizar página 1 de 14
Gangliosidose GM1, Tipo I, Infantil — A Propósito de 8 Casos
Cabral, Aguinaldo; Tasso, Teresa; Eusébio, Filomena; Gaspar, Ana; Charlton, Joanne; Marques dos Santos, Henriqueta; Moura-Nunes, J. F.São apresentados 8 doentes com Gangliosidose GM1 Tipo I: 3 do sexo masculino, 5 do feminino; cinco são de etnia cigana nascidos de casamentos consanguíneos. O diagnóstico ocorreu entre os 3-13 meses de idade (média: 5,6).Observou-se alta incidência de edema neonatal (7/8), anasarca (5/8), ascite (1/8) e predominância étnica não descrita.A dismorfia facial e esquelética, a organomegália, a hipotonia inicial e hi...
Doença de Armazenamento dos Ésteres do Colesterol. A Propósito de Dois Casos
Sequeira, Sílvia; Tasso, Teresa; Eusébio, Filomena; Cunha, Luís; Lopes, Ana Isabel; Moura Nunes, J. F.; Santos, Henriqueta Marques dosA doença de armazenamento dos ésteres do colesterol resulta da deficiência da lipase ácida lisosomial. É uma doença habitualmente caracterizada por hepatomegália e hiperlipidémia, por vezes pouco marcados, podendo ser diagnosticada apenas na idade adulta. Os dois casos clínicos que descrevemos revelam a grande variabilidade das manifestações clínicas desta situação considerada ainda relativamente rara.
Satellite-derived estimation of environmental suitability for malaria vector de...
Benali, Akli; Nunes, J.P.; Freitas, F.B.; Sousa, C.A.; Novo, M.T.; Lourenço, P.M.; Lima, J.C.; Seixas, J.; Almeida, A.P.G.Malaria was endemic in Europe for more than two millennia until it was eradicated in the 1970s. Recent autochthonous cases registered in Greece have increased the awareness regarding the threat of malaria re-emergence in Southern Europe. Currently, the presence of competent vectors, suitable environmental conditions and the evidences of a changing climate may increase the widespread re-emergence of malaria in S...
Cerebral venous thrombosis: an unexpected complication from spinal surgery
Costa, BL; Shamasna, M; Nunes, J; Magalhães, F; Peliz, AJPURPOSE: To provide new insights into the pathophysiology, prevention and diagnosis of cerebral venous thrombosis (CVT) associated with iatrogenic cerebrospinal fluid (CSF) leaks and/or external CSF drainage. METHODS: Case report and literature review. RESULTS: We describe the case of a 30-year-old woman who developed a CSF fistula after lumbar spinal surgery. The treatment included rest, hydration, caffeine, a...
The “montado”: determinant factor affecting the carcass characteristics and the...
Freitas, A.B.; Neves, J.; Nunes, J.T.; Almeida, J.A.The objective of this study was to assess the effect of the finishing system (under montanheira or with commercial feed) on carcass characteristics and dry cured-ham of Alentejano pigs. 24 pigs were fattening until 130 kg LW under montanheira and 24 pigs were fattening with commercial feed. Carcasses of pigs fattened under the montanheira system were slightly heavy (98,38 vs 96,13 kg), with significantly higher...
Diferenciação de isolados bacterianos com base no gene de Fe-hidrogenases
Pereira, Catarina; Nunes, J.; Rocha, Melissa; Moura, PatríciaO processo fermentativo de producao de H2 por microrganismos depende fundamentalmente da presenca de metaloenzimas designadas por hidrogenases. As hidrogenases sao enzimas envolvidas no metabolismo do H2, capazes de produzir ou consumir hidrogenio molecular, em processos relacionados com a transferencia de electroes e obtencao de energia. Elas catalisam a reaccao reversivel: H2 . 2H++ 2e- [1]. As hidrogenases d...
Improving the dynamical behaviour of a laser cutting equipment by using a carbo...
Vieira, D. G.; Meireles, José F.; Nunes, J. P.In order to improve the dynamic behaviour of an industrial laser cutting equipment a sandwich solution, using a carbon fibre reinforced polymer (CFRP) and polyester foam core, was implemented to construct its main runway structural frame, which supports the cutting head and major laser beam mirrors and lens. Nowadays, the commercial competiveness of laser cutting equipments is considerable enhanced by their hig...
Production of thermoplastic matrix towpregs for highly demanding and cost-effec...
Nunes, J. P.; Silva, J. F.This work reviews the work made in last years to produce thermoplastic matrix towpregs to highly demanding and more cost-effective commercial applications using a powder coating technology developed in Portugal by Minho and Porto Universities. Different thermoplastic matrices and continuous fibre reinforcements were used in the towpregs produced for highly demanding markets (e.g., carbon fibre reinforced Primos...
Processing conditions and properties of continuous fiber reinforced GF/PP therm...
Nunes, J. P.; Silva, J. F.; Novo, Paulo; Marques, A. T.The aim of the present work was to study and compare the processing conditions and final mechanical properties of continuous glass-fiber reinforced polypropylene composites (GF/PP) manufactured by using available thermoplastic preimpregnated materials produced by different methods.To assess the quality of the three different GF/PP pre-impregnated materials, final manufactured composite parts were submitted to m...
Composite pressure vessels for commercial applications
Nunes, J. P.; Oliveira, Luís; Silva, J. F.; Barros, B.; Amorim, Luís Manuel Machado de; Vasconcelos, M.A new generation of composite pressure vessels for large scale market applications has been studied in this work. The vessels consist on a plastic liner wrapped with a filament winding glass fibre reinforced polymer matrix structure. A polyethylene (PE) was selected as liner for water at room temperatures applications and a thermosetting resin was used as matrices in the glass reinforced filament wound laminate...
| Financiadores do RCAAP | |||||||
|
|
|
|
|
|
||