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Metodologia de Diagnóstico e Controlo de Evolução da Hepatite Aguda na Criança

Peutz-Jeghers syndrome: variability of gastrointestinal expression at pediatric...

Peutz-Jeghers syndrome is a rare autosomal dominant condition, characterized by gastrointestinal polyposis, mucocutaneous pigmentation and high risk of neoplasia in multiple organs. At pediatric age, major clinical impact is related to complications associated to intestinal polyps, but neoplasic risk isn't negligible. Though clinical surveillance is recommended since the age of 10 years, relevant lesions may oc...