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Um Caso Grave de Doença de Rendu-Osler-Weber

F. Pereira, Luísa; Tasso, Teresa; Portela, Regina; Cabral, Aguinaldo; Eusébio, Filomena; Aguas, Bárbara; Campos, Jorge; Gomes, Leonor B.

Os autores apresentam um caso de Doença de Rendu-Osler-Weber com evolução particularmente grave, numa adolescente de 16 anos.Trata-se de uma doente do sexo feminino, em que foi detectada acidentalmente, aos três anos de idade, hepatomegália. Os estudos subsequentesmostraram fibrose hepática e, posteriormente, fístulas artériovenosas cerebrais e fístulas artériovenosas pulmonares com insuficiência respiratóriaim...

Data: 2014   |   Origem: Acta Pediátrica Portuguesa

Spine Neuroimaging: Computed Tomography Diagnostic Signs

Barata Tavares, Joana; Santos, Carolina M; Cordeiro, Inês; Reimão, Sofia; Campos, Jorge G

Introduction: Computed tomography (CT) scans of the spine are among the most frequently performed neuroradiologic exams, studying several pathologies namely degenerative diseases. Specific signs in spine imaging initially described in conventional radiology can be applied to CT scans. The main goal of this work was their identification and characterization. Methods: A review of the main imagiological signs in C...

Data: 2012   |   Origem: Acta Médica Portuguesa

Diffusion-weighted MR Imaging Characterization of Progressive Multifocal Leucoe...

Barata Tavares, Joana; Geraldo, Ana F; Neto, Lia; Reimão, Sofia; Campos, Jorge G

Introduction: Progressive multifocal leucoencefalopathy (PML) is a subacute demielinating disease of the Central Nervous System caused by the neurotropic virus John Cunningham (JC), common in immunodeficient patients, namely in HIV infection. PML encephalic lesions have a progressive nature that needs characterization and progressive study, especially for evaluating the therapeutic response. Material and Method...

Data: 2012   |   Origem: Acta Médica Portuguesa

Acute Cerebellitis in Children: Regarding Different Etiologies

Mendes Dos Santos, Carolina; Sá, Graça; Geraldo, Ana Filipa; Tavares, Joana B; Neto, Lia; Campos, Jorge G

Acute cerebellitis is usually infectious, post-infectious or post-vaccination. Rarer causes include toxic ones. The clinical presentation is usually benign, however, severe cases with brainstem compression may present as coma. Regarding three pediatric clinical cases, the authors make a brief review on this entity, with particular emphasis on its causes and imaging findings. Case Reports: Three cases of pediatr...

Data: 2012   |   Origem: Acta Médica Portuguesa

Benign Fibro-osseous Lesions of the Craniofacial Complex with Aneurysmal Bone C...

Geraldo, Ana Filipa; Mendes dos Santos, Carolina; Tavares, Joana; Fernandes Sousa, Rita; Campos, Alexandre; Farias, João Paulo; Pimentel, José

Aneurysmal bone cyst are controversial osteolytic benign expansive lesions which occur more frequently in the metaphysis of long bones and spine. They are classified as primary or secondary lesions depending on the presence or absence of an associated bone pathology. The engraftment of aneurysmal bone cyst onto benign fibro-osseous lesions is established. However, in the craniofacial complex this combined lesio...

Data: 2012   |   Origem: Acta Médica Portuguesa

MRI Findings in Rasmussen’s Encephalitis

Mendes Dos Santos, Carolina; Moreno, Teresa; Sá, Graça; Rodrigues, David; Campos, Jorge G

Introduction: Rasmussen’s encephalitis is a chronic inflammatory encephalitis of unknown etiology. Clinical, imaging and electroencephalographic characteristic findings allow its diagnosis. Serial brain MRI evaluation of these patients has a characteristic pattern of temporal evolution. Regarding a clinical case, the authors make a brief review of this pathology, with particular emphasis on the MRI findings. Ca...

Data: 2012   |   Origem: Acta Médica Portuguesa

The contribution of perfusion CT in stroke.

Lopes, Leonor; Sousa, Rita; Ruivo, Joana; Reimão, Sofia; Sequeira, Paulo; Campos, Jorge

Multisection computed tomography (MSCT) was introduced in 1998 and improved neuroimaging quality, in particular concerning acute stroke. Previously, non-enhanced CT was used not only to detect early stroke signs, but also to exclude hemorrhage and non-vascular pathology responsible for the acute neurological deficit. Nowadays, using Perfusion CT (PCT) it is possible to obtain a functional study of the cerebral ...

Data: 2006   |   Origem: Acta Médica Portuguesa

Adult cerebellar medulloblastoma: imaging findings in eight cases.

Sousa, Rita; Sá, Graça; Reimão, Sofia; Lopes, Leonor; Ruivo, Joana; Albuquerque, Luísa; Campos, Jorge

Medulloblastoma is a brain tumor of neuroepithelial origin, frequent in children but rare in adults. The imaging pattern is well studied in the pediatric group thought there is controversy about the imaging characteristics in adults. We report CT and MRI imaging findings of 8 adult patients with cerebellar medulloblastoma. The mean age was 29.6 years (16-65 years). The male: female rate was 5:3. Most were later...

Data: 2006   |   Origem: Acta Médica Portuguesa

Spontaneous intracranial hypotension syndrome.

Sousa, Rita; Gouveia, Raquel; Lopes, Leonor; Ruivo, Nuno; Henriques, Nuno; Sá, Graça; Coutinho, David; Campos, Jorge

Spontaneous Intracranial Hypotension is a rare syndrome, characterized by orthostatic headaches, low CSF pressure and characteristic aspects on MRI. The authors describe a clinical case of Spontaneous Intracranial Hypotension, in which the MRI investigation revealed a low position of the cerebellar tonsils, a diffuse and symmetric dural enhancement and an engorgement of the cervical epidural venous plexus. The ...

Data: 2003   |   Origem: Acta Médica Portuguesa

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    Financiadores do RCAAP

Fundação para a Ciência e a Tecnologia Universidade do Minho   Governo Português Ministério da Educação e Ciência Programa Operacional da Sociedade do Conhecimento União Europeia