Inflammatory myopathies are systemic autoimmune diseases characterized by chronic muscle inflammation of unknown etiology. Clinically, there is reduced muscle strength and endurance. Its treatment is mainly pharmacological, including corticoids and imunossupressants. The intervention of Physical and Rehabilitation Medicine intends to prevent complications, to optimize function, to promote autonomy in daily acti...
Os autores apresentam um caso clínico de Artrite Idiopática Juvenil (A.LJ) - forma sistémica (Doença de Still), em criança do sexo feminino de 9 meses de idade, a propósito do qual fazem algumas considerações acerca do diagnostico, evolução clínica e terapêutica desta doença.
Os autores descrevem o caso clínico de uma criança do sexo feminino, de 2 anos e 9 meses de idade, que inicia em Julho/99, de forma insidiosa, dorso-lombalgia não acompanhada de sintomas constitucionais. Por persistência e agravamento progressivo das queixas álgicas, foi internada no Departamento de Pediatria do H. S. João em Setembro/99. Ao exame objectivo, evidenciava-se rigidez lombar acentuada, com mobiliza...
Introduction: Chemical synoviorthesis (CS) is a procedure frequently utilized/used in the management of patients with active arthritis in a limited number of joints. This technique involves the intraarticular administration of a therapeutic agent, such as long-acting corticosteroid. Its use in children is described since 1979. Currently, it is recommended in the oligoarticular form of juvenile idiopathic arthri...
Medicina ; Doctoral Programme in Medicine
Relapsing Polycondritis is a rare connective tissue disease of unknown aetiology that is manifested by inflammatory changes in cartilaginous tissues but the immune damage can spread and involve other tissues.Six patients with relapsing poycondritis treated in our service, between 1990 and 2003, were reviewed. The clinical features, age of onset, time from onset to diagnosis, disease associations and treatment w...
Lipoma arborescens is a rare intraarticular lesion of unknown etiology. The disorder usually presents as painless swelling and recurrent joint effusion. It is typically located in the knee (especially the suprapatellar bursa), though it has also been described in other joints. Laboratory test results are normal, as well as aspirated synovial fluid. Synovectomy is curative in most cases. The authors report a rev...
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