Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangiol...

• Author(s): Pontes, M ; Barbosa, C ; Coelho, ML ; Carvalho, L
• Date: 2013
• Persistent ID: http://hdl.handle.net/10400.4/1599
• Origin: Repositório do Centro Hospitalar e Universitário de Coimbra
• Subject(s): Linfangioleiomiomatose; Linfangiomioma
• Document Type: Article
• Language: Portuguese

Description

A 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.