Strength, muscle quality and functional capacity in liver transplanted familial...

• Author(s): Tomás, Mª Teresa ; Santa-Clara, Helena ; Monteiro, Estela ; Pimenta, Nuno ; Cabri, Jan ; Freire, António ; Barroso, Eduardo
• Date: 2009
• Persistent ID: http://hdl.handle.net/10400.21/289
• Origin: Repositório Científico do Instituto Politécnico de Lisboa
• Subject(s): Fisioterapia; Reabilitação; Polineuropatia amiloidótica familiar; Transplante de órgãos; Fígado; Massa muscular
• Document Type: Conference Object
• Language: English

Description

Liver transplantation is the unique treatment for several end-stage diseases. Familial Amiloidotic Polineuropathy (FAP) is a neurodegenerative disease related with systemic deposition of amyloidal fiber mainly on peripheral nervous system, clinically translated by an autonomous sensitive-motor neuropathy with severe functional limitations in some cases. The unique treatment for FAP disease is a liver transplant with a very aggressive medication to muscle metabolism and force production. To our knowledge there are no quantitative characterizations of body composition, strength or functional capacity in this population.