Ictal SPECT in Sturge-Weber syndrome

• Author(s): Bilgin, O ; Vollmar, C ; Peraud, A ; la Fougere, C ; Beleza, P ; Noachtar, S
• Date: 2008
• Persistent ID: http://hdl.handle.net/10400.23/447
• Origin: Repositório Científico do Hospital de Braga
• Subject(s): Síndrome de Sturge-Weber; Convulsões; Tomografia de Emissão de Fotão Único
• Document Type: Article
• Language: English

Description

We report on a patient with right-sided Sturge-Weber syndrome (SWS), in whom earlier functional hemispherectomy failed. Subtraction of ictal and interictal single-photon-emission-computed-tomography (SPECT) superimposed on individual MRI showed a right fronto-orbital hyperperfusion, with a left-sided EEG seizure pattern. Ictal SPECT supported our assumption that right frontal originated seizure pattern propagated to left hemisphere via the remaining right frontal bridge. Right orbito-frontal resection and disconnection from corpus callosum resulted in seizure freedom.